It may be the first manifestation of a renal angiomyolipoma aml, or rupture of renal artery or intraparenchymal aneurysm. Obstructed hemivagina with uterus didelphys and ipsilateral renal anomaly ohvira syndrome, formerly known as herlynwernerwunderlich syndrome, is a rare congenital malformation that involves abnormal development of the mullerian and wolffian ducts during the development of genitalia in female embryos. If you have access to a journal via a society or association membership, please browse to your society journal, select an article to view, and follow the instructions in this box. Obstructed hemivagina and ipsilateral renal anomaly ohvira, also known as herlynwernerwunderlich syndrome, is a rare syndrome with only a few hundred reported cases described since 1922.
Herlynwernerwunderlich syndrome radiology reference. It is most commonly diagnosed in puberty due to pelvic and abdominal pain, but more rarely it can present in neonates or adults, with primary infertility, pyometra, urinary obstruction and. Clinical presentation wunderlich syndrome is clinically characterized by lenks triad. Wunderlich syndrome is spontaneous, nontraumatic kidney bleeding confined to the subcapsular and perirenal space. Nestor san martin urrutia 2 herlynwernerwunderlich sindrome. Herlynwernerwunderlich syndrome hwws is a rare variant of mullerian duct anomalies. Sindrome ohvira hemivagina obstruida y anomalia renal. Herlynwerner wunderlich syndrome is a rare congenital anomaly of the urogenital tract, which is characterized by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. The herlynwerner wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It is not to be confused with the wunderlich syndrome.
Spontaneous nontraumatic renal haemorrhage, or wunderlich s syndrome, is a rare but potentially lifethreatening event. Herlynwerner wunderlich hww syndrome is a rare congenital disorder in which there is uterus didelphys, obstructed hemivagina and renal agenesis lending its acronym, ohvira syndrome. Anatomically, hwws is characterized by three key anomalies of the female reproductive tract. Wunderlich syndrome unusual complication of spontaneous. Isselbcher k, braunwald e, wilson j, martin j, fauci.
Jul 15, 2011 the herlynwernerwunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. Herlynwernerwunderlich hww syndrome is a rare congenital disorder in which there is uterus didelphys, obstructed hemivagina and renal agenesis lending its acronym, ohvira syndrome. As maes em 44,7 por cento eram primigestas e em 29,3 por cento secundigestas e a. Spontaneous nontraumatic renal haemorrhage, or wunderlichs syndrome, is a rare but potentially lifethreatening event. Only a handful of these cases have been associated with pyocolpos. We present the case of a 63yearold man on clopidogrel who became haemodynamically unstable as a result of this condition. Angioembolisation revealed the unusual finding of active bleeding from multiple distinct subsegmental renal vessels, for which haemostasis was.
Wunderlich syndrome ws is a rare condition characterized by a nontraumatic spontaneous acute renal hemorrhage into the subcapsular and perirenal spaces, found and described in this case. It is most commonly diagnosed in puberty due to pelvic and abdominal pain, but more rarely it can present in neonates or adults, with primary infertility. Tickoo, anuradha gopalan, pathologic features of renal cortical tumors, urol clin n am 35 2008 551561 links 11. Access to society journal content varies across our titles.
Obstructed hemivagina, didelphys uterus and ipsilateral renal agenesis. Herlynwernerwunderlich hww syndrome, is a rare anomaly characterized by mullerian duct anomalies mda associated with mesonephric duct anomalies 3. Wunderlich syndrome is a rare condition, in which spontaneous nontraumatic renal hemorrhage occurs into the subcapsular and perirenal spaces 2. Fernanda lopes percope 1, jose henrique withers aquino 2. Utero didelfo con hemivagina ciega y agenesia renal homolateral.
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